A 16-Year-Old Male with Cystic Fibrosis Is Admitted to the Inpatient

question 11

Multiple Choice

A 16-year-old male with cystic fibrosis is admitted to the inpatient pulmonary unit. He has been hospitalized several times in the past year with respiratory infections, including Pseudomonas and H. influenza. Because of his thick mucous, airway inflammation, and immobile mucosal cilia, microorganisms are unable to be effectively cleared from his lungs. He is supposed to perform vigorous airway mucous clearance measures at home with a vibrating vest and IPV (intrapulmonary percussive ventilation) device. However, the patient states that his treatment takes hours and he does not always feel sick. He estimates his compliance with home airway clearance regimen to be less than 50%.
-The patient asks the nurse to explain to him why he keeps getting sick from the same bacteria.Which of the following statements is the most appropriate response? 

• A)Your lungs produce these organisms because your cilia are permanently damaged.
• B)Your mucus traps and harbors the microorganisms and when they can't be cleared,they begin to breach your second and third lines of defense.
• C)Your disease stunts your immunity,so you are unable to fight those bacteria.
• D)You don't have second and third line defenses because of your cystic fibrosis.

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Definitions:

Avascular

Characterized by or pertaining to tissues that do not contain blood vessels; often referring to areas where healing may be impaired due to lack of blood flow.

Epidermal Layers

The layers of the epidermis, the outermost part of the skin, responsible for skin water resistance and barrier protection.

Lucidum

A thin, translucent layer of the epidermis located beneath the stratum corneum, primarily found in the palms of the hands and soles of the feet.

Granulosum

The granular layer of the epidermis, characterized by keratinocytes that contribute to the skin's barrier function.