What Is the Correct Code for Maple Syrup Urine Disease

question 6

Multiple Choice

What is the correct code for maple syrup urine disease?

• A) E71.0
• B) E71.1
• C) E71.110
• D) E71.120

---

Definitions:

Cataplexy

Episodes of sudden loss of muscle tone lasting under 2 minutes, triggered by laughter or joking in people who have had narcolepsy for a long time.

Muscle Tone

The continuous and passive partial contraction of the muscles, or the muscle's resistance to passive stretch during resting state.

Sleep Paralysis

A temporary inability to move or speak while falling asleep or upon waking, often accompanied by hallucinations.

Narcolepsy

Sleep disorder characterized by irresistible attacks of sleep plus (1) cataplexy or (2) recurrent intrusions of elements of rapid eye movement (REM) sleep into the transition between sleep and wakefulness.